Please use this identifier to cite or link to this item:
http://hdl.handle.net/20.500.12188/29848
Title: | Anesthetic Challenges And Management In Patient With Ataxia-Telangiectasia | Authors: | Jovanovski Srceva, Marija Kondov, Goran Kartalov, Andrijan Georgiev, Antonio Kuzmanovski, Igor Osmani, Bujar Andov, Mishel Gavrilovska-Brzanov Aleksandra Jakupi, Nexhati Stevic, Marija Stojanoski, Sinisha |
Keywords: | Ataxia-telangiectasia Anesthesia Management One lung ventilation |
Issue Date: | 1-Dec-2023 | Publisher: | Walter de Gruyter GmbH | Journal: | Prilozi = Contributions | Abstract: | Louis-Bar Syndrome is a synonym for a very rare complex neurodegenerative disorder ataxia-telangiectasia (A-T). This is an autosomal recessive inherited disease that encompasses abnormalities in the cerebellum, multisystem degeneration, immunodeficiency, increased risk for malignancy and consecutive respiratory insufficiency. Most of the patients are radiosensitive and any exposing to ionization may lead to progression of the disease. Potential risks from anesthesia, mechanical ventilation, and postoperative complications in these patients have been insufficiently discussed in the literature. We present a successful anesthetic and respiratory management with one-lung ventilation in a patient with Louis-Bar Syndrome who underwent video assisted thoracoscopy (VATS) for recurrent pleural effusion. | URI: | http://hdl.handle.net/20.500.12188/29848 | DOI: | 10.2478/prilozi-2023-0048 |
Appears in Collections: | Faculty of Medicine: Journal Articles |
Show full item record
Items in DSpace are protected by copyright, with all rights reserved, unless otherwise indicated.